Interstitial Pneumonia with Autoimmune Features - Management

IMMUNOSUPPRESSANTS:⁴

Although there are no currently approved therapies, corticosteroids or steroid-sparing immunosuppressants are often empirically used to treat IPAF.

LUNG TRANSPLANTATION:⁵

Typically used as a life-saving approach in patients with end-stage CTD-ILD.

SUPPORTIVE CARE:⁶

Supplemental Oxygen.