Mixed Connective Tissue Disease-related ILD
MCTD-ILD DIAGNOSTICS
FOR MCTD1,7 | FOR MCTD-RELATED ILD2,8,9 | ||
---|---|---|---|
Established diagnosis of MCTD OR comprehensive medical history + physical exam + serologies (anti-U1- RNP, ANA, RF). |
PFTs | HRCT | Lung Biopsy |
Restrictive defect with reduced DLco. | Fibrotic NSIP UIP |
Not always necessary |