SYSTEMIC SCLEROSIS-RELATED ILD - DIAGNOSIS

DIAGNOSIS7

Symptoms

  • Calcinosis
  • Raynaud’s phenomenon
  • Articular involvement
  • Esophageal dysmotility
  • Lung fibrosis
  • Isolated pulmonary arterial hypertension
  • Heart involvement
  • Renal crisis

SSc-ILD: Diagnosis

FOR SSc3,7,8,13 FOR SSc-ILD8,14-17
Established diagnosis of SSc
OR
Clinical history + physical exam + serologies (e.g., anti-Scl-70; anti-U3RNP, anti-Th/To)
PFTs HRCT Lung Biopsy
Restrictive defect (or mixed, if other comorbidities present) NSIP
  UIP also seen but rarer
NSIP (mostly)
Lung biopsy not commonly performed

See also

Test your Knowledge
Test your knowledge

Take the test

Lung X-Ray Example
Rad Rounds Mobile App

Download the app

Interstitial lung disease in systemic sclerosis with a focus on chest CT

Media Library

See Media