The interstitial lung diseases have similar symptoms, physiology, radiology, and histopathology, which may make the process of diagnosis difficult, even for ILD experts.27 Due to the significant overlap between these features, a collaborative, multidisciplinary approach to diagnosis is recommended for any patient suspected of having interstitial lung disease.5 It is important to integrate clinical findings seen by a pulmonologist and/or rheumatologist with radiographic and pathologic diagnoses to confirm the final diagnosis.45

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Idiopathic Pulmonary Fibrosis (an Update) and Progressive Pulmonary Fibrosis in Adults: An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline

Reference

5. Raghu G, Collard HR, Egan JJ, et al. An official ATS/ERS/JRS/ALAT statement: idiopathic pulmonary fibrosis: evidence-based guidelines for diagnosis and management. Am J Respir Crit Care Med. 2011;183:788-824.

27. Raghu G, Brown KK. Interstitial lung disease: clinical evaluation and keys to an accurate diagnosis. Clin Chest Med. 2004;25:409-419.

45. Raghu G, Remy-Jardin M, Myers JL, et al. Diagnosis of Idiopathic Pulmonary Fibrosis. An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline. Am J Respir Crit Care Med. 2018;198(5):e44-e68.